Isovaleryl-l-carnitine

Isovaleryl-l-carnitine is a lipid of Fatty Acyls (FA) class.

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There are no associated biomedical information in the current reference collection.

Current reference collection contains 79 references associated with Isovaleryl-l-carnitine in LipidPedia. Due to lack of full text of references or no associated biomedical terms are recognized in our current text-mining method, we cannot extract any biomedical terms related to diseases, pathways, locations, functions, genes, lipids, and animal models from the associated reference collection.

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All references with Isovaleryl-l-carnitine

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Authors Title Published Journal PubMed Link
Couce ML et al. Genotype and phenotype characterization in a Spanish cohort with isovaleric acidemia. 2017 J. Hum. Genet. pmid:27904153
Alexandre-Gouabau MC et al. Maternal and cord blood LC-HRMS metabolomics reveal alterations in energy and polyamine metabolism, and oxidative stress in very-low birth weight infants. 2013 J. Proteome Res. pmid:23527880
Malaguarnera M Carnitine derivatives: clinical usefulness. 2012 Curr. Opin. Gastroenterol. pmid:22333562
van Calcar SC et al. 2-methylbutyryl-CoA dehydrogenase deficiency in Hmong infants identified by expanded newborn screen. 2007 WMJ pmid:17393751
Bene J et al. Changes of plasma fasting carnitine ester profile in patients with ulcerative colitis. 2006 World J. Gastroenterol. pmid:16440427
Fries MH et al. Isovaleric acidemia: response to a leucine load after three weeks of supplementation with glycine, L-carnitine, and combined glycine-carnitine therapy. 1996 J. Pediatr. pmid:8804338
Salamino F et al. Involvement of erythrocyte calpain in glycine- and carnitine-treated isovaleric acidemia. 1994 Pediatr. Res. pmid:7970932
Miotto G et al. Control of hepatic proteolysis by leucine and isovaleryl-L-carnitine through a common locus. Evidence for a possible mechanism of recognition at the plasma membrane. 1992 J. Biol. Chem. pmid:1429558
Shigematsu Y et al. Prenatal diagnosis of isovaleric acidemia by fast atom bombardment and tandem mass spectrometry. 1991 Clin. Chim. Acta pmid:1777996
Chalmers RA et al. Urinary excretion of l-carnitine and acylcarnitines by patients with disorders of organic acid metabolism: evidence for secondary insufficiency of l-carnitine. 1984 Pediatr. Res. pmid:6441143

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