Huemer M et al. |
Newborn screening for homocystinurias and methylation disorders: systematic review and proposed guidelines. |
2015 |
J. Inherit. Metab. Dis. |
pmid:25762406
|
Shigematsu Y et al. |
Useful second-tier tests in expanded newborn screening of isovaleric acidemia and methylmalonic aciduria. |
2010 |
J. Inherit. Metab. Dis. |
pmid:20440648
|
Kuhara T et al. |
Gas chromatographic-mass spectrometric newborn screening for propionic acidaemia by targeting methylcitrate in dried filter-paper urine samples. |
2002 |
J. Inherit. Metab. Dis. |
pmid:12118533
|
Wang F et al. |
Clinical, biochemical, and molecular analysis of combined methylmalonic acidemia and hyperhomocysteinemia (cblC type) in China. |
2010 |
J. Inherit. Metab. Dis. |
pmid:20924684
|
Broderick TL et al. |
L-propionylcarnitine enhancement of substrate oxidation and mitochondrial respiration in the diabetic rat heart. |
1996 |
J. Mol. Cell. Cardiol. |
pmid:8729065
|
Kotaka K et al. |
Reversal of ischemia-induced mitochondrial dysfunction after coronary reperfusion. |
1982 |
J. Mol. Cell. Cardiol. |
pmid:7108975
|
Ferrari R et al. |
Prolonged propionyl-L-carnitine pre-treatment of rabbit: biochemical, hemodynamic and electrophysiological effects on myocardium. |
1992 |
J. Mol. Cell. Cardiol. |
pmid:1625347
|
Perna AF et al. |
L-Propionyl carnitine, homocysteine and S-adenosylhomocysteine in hemodialysis. |
2007 Jan-Feb |
J. Nephrol. |
pmid:17347975
|
Bogusiewicz A et al. |
In HepG2 cells, coexisting carnitine deficiency masks important indicators of marginal biotin deficiency. |
2015 |
J. Nutr. |
pmid:25527659
|
Brass EP and Ruff LJ |
Effect of carnitine on propionate metabolism in the vitamin B-12--deficient rat. |
1989 |
J. Nutr. |
pmid:2778544
|
Marble M et al. |
Neonatal vitamin B12 deficiency secondary to maternal subclinical pernicious anemia: identification by expanded newborn screening. |
2008 |
J. Pediatr. |
pmid:18410783
|
Cunningham VJ et al. |
Uptake of [N-methyl-11C]propionyl-L-carnitine (PLC) in human myocardium. |
1996 |
J. Pharmacol. Exp. Ther. |
pmid:8613961
|
Hotta N et al. |
Effect of propionyl-L-carnitine on motor nerve conduction, autonomic cardiac function, and nerve blood flow in rats with streptozotocin-induced diabetes: comparison with an aldose reductase inhibitor. |
1996 |
J. Pharmacol. Exp. Ther. |
pmid:8558455
|
Wu X et al. |
Functional characteristics and tissue distribution pattern of organic cation transporter 2 (OCTN2), an organic cation/carnitine transporter. |
1999 |
J. Pharmacol. Exp. Ther. |
pmid:10454528
|
Mancinelli A et al. |
Uptake of L-carnitine and its short-chain ester propionyl-L-carnitine in the isolated perfused rat liver. |
2005 |
J. Pharmacol. Exp. Ther. |
pmid:15951397
|
Safarinejad MR et al. |
Comparison of vitamin E and propionyl-L-carnitine, separately or in combination, in patients with early chronic Peyronie's disease: a double-blind, placebo controlled, randomized study. |
2007 |
J. Urol. |
pmid:17706714
|
Alvarez de Sotomayor M et al. |
Effect of L-carnitine and propionyl-L-carnitine on endothelial function of small mesenteric arteries from SHR. |
2007 |
J. Vasc. Res. |
pmid:17483601
|
Cipolla MJ et al. |
Propionyl-L-carnitine dilates human subcutaneous arteries through an endothelium-dependent mechanism. |
1999 |
J. Vasc. Surg. |
pmid:10359944
|
Loffredo L et al. |
Imbalance between nitric oxide generation and oxidative stress in patients with peripheral arterial disease: effect of an antioxidant treatment. |
2006 |
J. Vasc. Surg. |
pmid:16950429
|
Sarafoglou K et al. |
Expanded newborn screening for detection of vitamin B12 deficiency. |
2011 |
JAMA |
pmid:21427371
|
Signorelli SS et al. |
Propionyl-L-carnitine therapy: effects on endothelin-1 and homocysteine levels in patients with peripheral arterial disease and end-stage renal disease. |
2006 |
Kidney Blood Press. Res. |
pmid:16809937
|
Mister M et al. |
Propionyl-L-carnitine prevents renal function deterioration due to ischemia/reperfusion. |
2002 |
Kidney Int. |
pmid:11849462
|
Azzollini N et al. |
Propionyl-L-carnitine prevents early graft dysfunction in allogeneic rat kidney transplantation. |
2008 |
Kidney Int. |
pmid:19008910
|
Gómez-Amores L et al. |
Antioxidant activity of propionyl-L-carnitine in liver and heart of spontaneously hypertensive rats. |
2006 |
Life Sci. |
pmid:16263137
|
Bueno R et al. |
L-carnitine and propionyl-L-carnitine improve endothelial dysfunction in spontaneously hypertensive rats: different participation of NO and COX-products. |
2005 |
Life Sci. |
pmid:15958269
|
Hozyasz KK et al. |
Whole blood propionylcarnitine in newborns with orofacial cleft. |
2011 |
Matern Child Nutr |
pmid:21470367
|
Odiet JA et al. |
Carnitine palmitoyl transferase-I activity in the aging mouse heart. |
1995 |
Mech. Ageing Dev. |
pmid:7616763
|
Barker GA et al. |
Effect of propionyl-L-carnitine on exercise performance in peripheral arterial disease. |
2001 |
Med Sci Sports Exerc |
pmid:11528327
|
Ferrari R et al. |
Metabolic modulation and optimization of energy consumption in heart failure. |
2003 |
Med. Clin. North Am. |
pmid:12693736
|
Cotter MA et al. |
Effects of acetyl- and proprionyl-L-carnitine on peripheral nerve function and vascular supply in experimental diabetes. |
1995 |
Metab. Clin. Exp. |
pmid:7666797
|
Brass EP and Beyerinck RA |
Interactions of propionate and carnitine metabolism in isolated rat hepatocytes. |
1987 |
Metab. Clin. Exp. |
pmid:3110541
|
Riccioni C et al. |
Rehabilitative treatment in peripheral artery disease: protocol application and follow-up. |
2010 |
Minerva Cardioangiol |
pmid:20948502
|
Pekkinen J et al. |
Betaine supplementation causes increase in carnitine metabolites in the muscle and liver of mice fed a high-fat diet as studied by nontargeted LC-MS metabolomics approach. |
2013 |
Mol Nutr Food Res |
pmid:23868375
|
Löster H et al. |
Effects of L-carnitine and its acetyl and propionyl esters on ATP and PCr levels of isolated rat hearts perfused without fatty acids and investigated by means of 31P-NMR spectroscopy. |
1999 |
Mol. Cell. Biochem. |
pmid:10569188
|
Broderick TL et al. |
Propionyl-L-carnitine effects on postischemic recovery of heart function and substrate oxidation in the diabetic rat. |
2000 |
Mol. Cell. Biochem. |
pmid:10839205
|
Cui J et al. |
Effects of L-carnitine and its derivatives on postischemic cardiac function, ventricular fibrillation and necrotic and apoptotic cardiomyocyte death in isolated rat hearts. |
2003 |
Mol. Cell. Biochem. |
pmid:14674702
|
Motterlini R et al. |
Functional and metabolic effects of propionyl-L-carnitine in the isolated perfused hypertrophied rat heart. |
1992 |
Mol. Cell. Biochem. |
pmid:1480142
|
Roe DS et al. |
Evidence for a short-chain carnitine-acylcarnitine translocase in mitochondria specifically related to the metabolism of branched-chain amino acids. |
2000 |
Mol. Genet. Metab. |
pmid:10655160
|
Davenport RJ et al. |
Propionyl-L-carnitine: labelling in the N-methyl position with carbon-11 and pharmacokinetic studies in rats. |
1995 |
Nucl. Med. Biol. |
pmid:8535330
|
Mingorance C et al. |
Pharmacological effects and clinical applications of propionyl-L-carnitine. |
2011 |
Nutr. Rev. |
pmid:21521230
|
Neri B et al. |
Differences between carnitine derivatives and coenzyme Q10 in preventing in vitro doxorubicin-related cardiac damages. |
1988 |
Oncology |
pmid:3368201
|
Chen PW et al. |
Stabilization of blood methylmalonic acid level in methylmalonic acidemia after liver transplantation. |
2010 |
Pediatr Transplant |
pmid:19686300
|
Kasahara M et al. |
Living-donor liver transplantation for propionic acidemia. |
2012 |
Pediatr Transplant |
pmid:22151065
|
Riva E and Leopaldi D |
Control of the cardiac consequences of myocardial ischemia and reperfusion by L-propionylcarnitine: age-response and dose-response studies in the rat heart. |
1993 |
Pediatr. Res. |
pmid:8255679
|
Chalmers RA et al. |
Urinary excretion of l-carnitine and acylcarnitines by patients with disorders of organic acid metabolism: evidence for secondary insufficiency of l-carnitine. |
1984 |
Pediatr. Res. |
pmid:6441143
|
Valoti M et al. |
Effects of carnitine and its derivatives on gastric acid secretion in rats. |
1996 Nov-Dec |
Pharmacol. Res. |
pmid:9076846
|
Caruso A et al. |
Protective effect of propionyl-L-carnitine against PAF-induced rat paw oedema. |
1995 |
Pharmacol. Res. |
pmid:7784308
|
Signorelli SS et al. |
Effects of ischaemic stress on leukocyte activation processes in patients with chronic peripheral occlusive arterial disease: role of L-propionyl carnitine administration. |
2001 |
Pharmacol. Res. |
pmid:11592865
|
Arafa HM and Sayed-Ahmed MM |
Protective role of carnitine esters against alcohol-induced gastric lesions in rats. |
2003 |
Pharmacol. Res. |
pmid:12860448
|
Marciani P et al. |
L-carnitine and carnitine ester transport in the rat small intestine. |
1991 |
Pharmacol. Res. |
pmid:2062791
|