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Cerebrotendinous xanthomatosis is treatable. |
1985 |
Pediatr Dermatol |
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On the structural specificity in the regulation of the hydroxymethylglutaryl-CoA reductase and the cholesterol-7 alpha-hydroxylase in rats. Effects of cholestanol feeding. |
1985 |
Biochim. Biophys. Acta |
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Plank L et al. |
Effect of sterol incorporation on head group separation in liposomes. |
1985 |
Chem. Phys. Lipids |
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Biosynthesis of cholestanol from bile acid intermediates in the rabbit and the rat. |
1985 |
J. Biol. Chem. |
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1985 |
J. Clin. Invest. |
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Biochemical diagnosis of cerebrotendinous xanthomatosis using reversed phase thin layer chromatography. |
1986 |
J. Biochem. |
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Effects of dietary triglycerides on serum and liver lipids and sterol excretion of rats. |
1986 |
J. Nutr. |
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Cholesterol precursor sterols, plant sterols, and cholestanol in human bile and gallstones. |
1986 |
Gastroenterology |
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Fecal bile acids and neutral sterols in rats with spontaneous colon cancer. |
1986 |
Int. J. Cancer |
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Minor and trace sterols from marine invertebrates 56. Novel coprostanols from the marine sponge Petrosia ficiformis. |
1986 |
Steroids |
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Differences in uptake and esterification of saturated analogues of cholesterol by rat small intestine. |
1986 |
Am. J. Physiol. |
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Parker F |
Normocholesterolemic xanthomatosis. |
1986 |
Arch Dermatol |
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Influence of peroral antibiotics upon the biotransformatory activity of the intestinal microflora in healthy subjects. |
1986 |
Eur. J. Clin. Invest. |
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Garraffo HM and Gros EG |
Biosynthesis of bufadienolides in toads. VI. Experiments with [1,2-3H]cholesterol, [21-14C]coprostanol, and 5 beta-[21-14 C]pregnanolone in the toad Bufo arenarum. |
1986 Sep-Oct |
Steroids |
pmid:3127947
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Salen G et al. |
Increased concentrations of cholestanol and apolipoprotein B in the cerebrospinal fluid of patients with cerebrotendinous xanthomatosis. Effect of chenodeoxycholic acid. |
1987 |
N. Engl. J. Med. |
pmid:3106810
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Lozano R et al. |
Metabolism of sterols of varying ring unsaturation and methylation by Caenorhabditis elegans. |
1987 |
Lipids |
pmid:3104715
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Relationship between fecal neutral steroid concentrations and malignancy in colon cells. |
1987 |
Cancer |
pmid:3111679
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van Faassen A et al. |
Bile acids, neutral steroids, and bacteria in feces as affected by a mixed, a lacto-ovovegetarian, and a vegan diet. |
1987 |
Am. J. Clin. Nutr. |
pmid:3120571
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Establishment of a biochemically active intestinal ecosystem in ex-germfree rats. |
1987 |
Appl. Environ. Microbiol. |
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Vahouny GV et al. |
Dietary fiber supplementation and fecal bile acids, neutral steroids and divalent cations in rats. |
1987 |
J. Nutr. |
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Shefer S et al. |
Competitive inhibition of bile acid synthesis by endogenous cholestanol and sitosterol in sitosterolemia with xanthomatosis. Effect on cholesterol 7 alpha-hydroxylase. |
1988 |
J. Clin. Invest. |
pmid:3143743
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Hirsch D et al. |
DSC, X-ray and NMR properties of cholesterol-cholestanol-dihydrate crystals. |
1988 |
Clin. Chim. Acta |
pmid:3133139
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Koivisto PV and Miettinen TA |
Plasma and biliary cholestanol related to steroid metabolism in familial hypercholesterolemia patients with and without ileal exclusion. |
1988 |
Clin. Chim. Acta |
pmid:3133140
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Midtvedt AC et al. |
Development of five metabolic activities associated with the intestinal microflora of healthy infants. |
1988 Jul-Aug |
J. Pediatr. Gastroenterol. Nutr. |
pmid:3135382
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Andriamiarina R et al. |
Effects of stigmasterol-supplemented diets on fecal neutral sterols and bile acid excretion in rats. |
1989 |
Ann. Nutr. Metab. |
pmid:2516429
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Bhattacharyya AK et al. |
Differences in fecal excretion of cholesterol and bacterial degradation products in high- and low-responding rhesus monkeys: implications in colon cancer. |
1989 |
Nutr Cancer |
pmid:2496397
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Nicolaides N et al. |
Meibomian gland dysfunction. III. Meibomian gland lipids. |
1989 |
Invest. Ophthalmol. Vis. Sci. |
pmid:2498228
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Ha TB and Djerassi C |
Minor and trace sterols in marine invertebrates. 62. Novel coprostanols with unusual side chains from the marine sponge Calyx nicaeensis. |
1989 Mar-May |
Steroids |
pmid:2508274
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Wolthers BG et al. |
Reduction of urinary bile alcohol excretion and serum cholestanol in patients with cerebrotendinous xanthomatosis after oral administration of deoxycholic acid. |
1990 |
Clin. Chim. Acta |
pmid:2282689
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Strandberg TE et al. |
Metabolic variables of cholesterol during squalene feeding in humans: comparison with cholestyramine treatment. |
1990 |
J. Lipid Res. |
pmid:2246614
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Midtvedt T et al. |
Intestinal microbial conversion of cholesterol to coprostanol in man. Influence of antibiotics. |
1990 |
APMIS |
pmid:2223037
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McKenna P et al. |
A case of cerebrotendinous xanthomatosis. II: The sterol content of a cataractous lens. |
1990 |
Br J Ophthalmol |
pmid:2285688
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Bencze KS et al. |
Magnetic resonance imaging of the brain and spinal cord in cerebrotendinous xanthomatosis. |
1990 |
J. Neurol. Neurosurg. Psychiatr. |
pmid:2107278
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Overturf ML et al. |
Dietary cholesterol absorption, and sterol and bile acid excretion in hypercholesterolemia-resistant white rabbits. |
1990 |
J. Lipid Res. |
pmid:2086701
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Kim KS et al. |
Effects of cholestanol feeding on corneal dystrophy in mice. |
1991 |
Biochim. Biophys. Acta |
pmid:1911869
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Dotti MT et al. |
Cerebrotendinous xanthomatosis as a multisystem disease mimicking premature ageing. |
1991 |
Dev. Neurosci. |
pmid:1817044
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Sziegoleit A and Linder D |
Studies on the sterol-binding capacity of human pancreatic elastase 1. |
1991 |
Gastroenterology |
pmid:1993499
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Kosaka D et al. |
Stable isotope dilution assay for 5 beta-cholestane-3 alpha,7 alpha,12 alpha,25-tetrol and 5 beta-cholestane-3 alpha,7 alpha,12 alpha,23,25-pentol in human serum using [26,27-D6] labeled internal standards; a highly accurate approach to the serological diagnosis of cerebrotendinous xanthomatosis. |
1991 |
Clin. Chim. Acta |
pmid:1934504
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Kuriyama M et al. |
High levels of plant sterols and cholesterol precursors in cerebrotendinous xanthomatosis. |
1991 |
J. Lipid Res. |
pmid:2066659
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Nakamura T et al. |
Combined treatment with chenodeoxycholic acid and pravastatin improves plasma cholestanol levels associated with marked regression of tendon xanthomas in cerebrotendinous xanthomatosis. |
1991 |
Metab. Clin. Exp. |
pmid:1908036
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Nikkilä K et al. |
High cholestanol and low campesterol-to-sitosterol ratio in serum of patients with primary biliary cirrhosis before liver transplantation. |
1991 |
Hepatology |
pmid:2010161
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Salen G et al. |
Biochemical abnormalities in cerebrotendinous xanthomatosis. |
1991 |
Dev. Neurosci. |
pmid:1817043
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Fujiyama J et al. |
Parkinsonism in cerebrotendinous xanthomatosis. |
1991 Mar-Apr |
Jpn. J. Med. |
pmid:1865593
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Nikkilä K et al. |
Serum and hepatic cholestanol, squalene and noncholesterol sterols in man: a study on liver transplantation. |
1992 |
Hepatology |
pmid:1568728
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Owen RW et al. |
Faecal steroids and colorectal cancer: steroid profiles in subjects with adenomatous polyps of the large bowel. |
1992 |
Eur. J. Cancer Prev. |
pmid:1463972
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Björkhem I et al. |
Mechanism and stereochemistry in the sequential enzymatic saturation of the two double bonds in cholesta-4,6-dien-3-one. |
1992 |
J. Biol. Chem. |
pmid:1400303
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Lee SP et al. |
Biliary sludge as a cause of acute pancreatitis. |
1992 |
N. Engl. J. Med. |
pmid:1734248
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Steinberg WM |
Acute pancreatitis--never leave a stone unturned. |
1992 |
N. Engl. J. Med. |
pmid:1734255
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Nikkilä K et al. |
Liver transplantation modifies serum cholestanol, cholesterol precursor and plant sterol levels. |
1992 |
Clin. Chim. Acta |
pmid:1499139
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Tokimura Y et al. |
Electrophysiological studies in cerebrotendinous xanthomatosis. |
1992 |
J. Neurol. Neurosurg. Psychiatr. |
pmid:1312580
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